๐”– Bobbio Scriptorium
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Fetal Krabbe leukodystrophy

โœ Scribed by J. J. Martin; J. G. Leroy; C. Ceuterick; J. Libert; P. Dodinval; L. Martin

Publisher
Springer-Verlag
Year
1981
Tongue
English
Weight
949 KB
Volume
53
Category
Article
ISSN
0001-6322

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Galactocerebrosidase (GALC) is a lysosomal b-galactosidase responsible for the hydrolysis of the galactosyl moiety from several galactolipids, including galactosylceramide and psychosine. The deficiency of this enzyme results in the autosomal recessive disorder called Krabbe disease. It is also call

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