Proteus syndrome is a rare hamartomatous disorder involving macrodactyly, hemihypertrophy, and subcutaneous lymphangiomas; fewer than 25 cases have been reported worldwide. We report a case of a thoracic epidural lymphangiolipoma in a 5-year-old boy with Proteus syndrome. Computerized axial tomograp
Expanding the phenotype of the Proteus syndrome: A severely affected patient with new findings
β Scribed by Mayatepek, Ertan ;Kurczynski, Thaddeus W. ;Ruppert, Elizabeth S. ;Hennessy, James R. ;Brinker, Ray A. ;French, Beatrice N.
- Publisher
- John Wiley and Sons
- Year
- 1989
- Tongue
- English
- Weight
- 643 KB
- Volume
- 32
- Category
- Article
- ISSN
- 0148-7299
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