The intracellular concentration of free leucine, isoleucine, and valine and their metabolism were studied in lymphoblast cultures established from peripheral blood of an individual with maple syrup urine disease (MSUD) and a control subject. Branched-chain alpha-keto acid decarboxylase activity in t
Evaluation of branched-chain amino acid intake in children with maple syrup urine disease and methylmalonic aciduria
β Scribed by H. G. Parsons; R. J. Carter; M. Unrath; F. F. Snyder
- Publisher
- Springer
- Year
- 1990
- Tongue
- English
- Weight
- 859 KB
- Volume
- 13
- Category
- Article
- ISSN
- 0141-8955
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