Erythropoietic protoporphyria, transfusion therapy and liver disease
β Scribed by D.J. TODD; M.E. CALLENDER; E.E. MAYNE; M. WALSH; D. BURROWS
- Book ID
- 108662298
- Publisher
- John Wiley and Sons
- Year
- 1992
- Tongue
- English
- Weight
- 306 KB
- Volume
- 127
- Category
- Article
- ISSN
- 0007-0963
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π SIMILAR VOLUMES
In erythropoietic protoporphyria (EPP), there is excessive production of protoporphyrin, primarily in the bone marrow, resulting in increased biliary excretion of this heme precursor. Some patients will develop progressive liver disease that may ultimately require liver transplantation. However, exc
Liver transplantation is an established lifesaving treatment for patients with severe protoporphyric liver disease, but disease recurrence in the graft occurs for the majority of recipients. Severe burn injuries may occur when protective light filters are not used with surgical luminaires. Motor neu