𝔖 Bobbio Scriptorium
✦   LIBER   ✦

Enzymatic study of GM1 gangliosidosis

✍ Scribed by Yutaka Toru; Okada Shintaro; Mimaki Koji; Sugita Takahiro; Yabuuchi Hyakuji


Book ID
115820562
Publisher
Elsevier Science
Year
1975
Tongue
English
Weight
523 KB
Volume
59
Category
Article
ISSN
0009-8981

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## Abstract Acid β‐galactosidase activity can be separated into multiple molecular forms by isoelectric focusing on cellulose acetate membranes. The residual acid β‐galactosidase in the juvenile form of G~M1~ gangliosidosis has three bands of enzyme activity with an apparent isoelectric pH (pI) ran

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