✦ LIBER ✦
Effect of splenectomy on destructive bone changes in children with chronic (Type I) Gaucher disease
✍ Scribed by A. Ashkenazi; R. Zaizov; Y. Matoth
- Publisher
- Springer
- Year
- 1986
- Tongue
- English
- Weight
- 469 KB
- Volume
- 145
- Category
- Article
- ISSN
- 0340-6997
No coin nor oath required. For personal study only.
✦ Synopsis
A premature infant with duplication of material from chromosome 11 and some features of the Beckwith-Wiedemann syndrome developed the bronze baby syndrome when exposed to phototherapy. He subsequently developed hepatocellular dysfunction and died aged 5 weeks. Post mortem examination revealed striking hypoplasia of intralobular bile ducts but little inflammatory change or necrosis in the liver.