𝔖 Bobbio Scriptorium
✦   LIBER   ✦

Effect of selenium compounds on selenium content, growth and 35S-cystine metabolism of skin fibroblasts from normal and cystinotic individuals

✍ Scribed by W.J. Rhead; J.A. Schneider


Book ID
104105987
Publisher
Elsevier Science
Year
1976
Weight
920 KB
Volume
6
Category
Article
ISSN
0006-3061

No coin nor oath required. For personal study only.

✦ Synopsis


_BSTRACT

Kidney samples from children with the inborn metabolic disease cystinosis contain 4 times more selenium (Se) than do kidney samples from normal individuals (p = 0.1). However. when cultured skin frbroblasts from cystinotic patients and normal control individuals are incubated in Se-D,L-me*&ionine, Se-D,L-cystine, Se-cystamine-HCl, Se-urea, selenite or in medium without added seIenium, only the cystinotic tibrobIasts grown in Se-urea or seIenite (SeOg) contain more selenium than do the corresponding normal cells (p < 0.05). In both types of cultured fibroblasts, the order of descending toxicity per ppm selenium is: Se-urea > Se-cystamine > Se-cystine > SeOg ) Semethionine. High (apparently toxic) concentrations of Se-urea and Secystamine lower the elevated intracelluiar free <nonprotein) cystine content of cystinotic fibroblasts to less than 60% of control values; at lower concentrations, these compounds raise the cystine content of these cells to over 140% of control values. Appropriate concentrations of SeOi, Se-cystine and Se-