Hereditary angioneurotic edema (HAE) is an autosomal dominant disorder characterized by episodic local subcutaneous and submucosal edema caused by the deficiency of activated C1 esterase inhibitor protein (C1-INH, type I (C1NH): reduced serum antigen level, type II: reduced activity and normal serum
Effect of danazol on dysfunctional C 1 inhibitor in a patient with angioedema
✍ Scribed by Peter Michael Kövary; Wolfgang Opferkuch; Karin Echternacht-Happle; Rudolf Happle
- Publisher
- Springer-Verlag
- Year
- 1981
- Tongue
- English
- Weight
- 335 KB
- Volume
- 270
- Category
- Article
- ISSN
- 0340-3696
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Communicated by Mark H. Paalman Hereditary angioedema (HAE) is a disorder characterised by recurrent attacks of localized subcutaneous or submucosal edema. It is inherited in an autosomal dominant fashion and caused by a deficiency of C1 inhibitor (C1 inh, or C1NH). Most patients with HAE have an ab
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