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Diffuse myocardial fibrosis in pediatric hypertrophic cardiomyopathy

✍ Scribed by Tarique Hussain, Andrea Dragulescu…


Book ID
120924190
Publisher
BioMed Central
Year
2013
Tongue
English
Weight
190 KB
Volume
15
Category
Article
ISSN
1097-6647

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Desmin-related myopathy (DRM) is known to cause different types of cardiomyopathy. Late gadolinium enhancement cardiovascular magnetic resonance (CMR) has been shown to identify fibrosis in ischemic and non-ischemic cardiomyopathies. We present a rare case of desmin-related hypertrophic cardiomyopat