Cranial fasciitis of childhood

✍ Scribed by Margarita Larralde; Paula Boggio; Roberto Schroh; Humberto Cusumano

• Book ID: 104463891
• Publisher: John Wiley and Sons
• Year: 2003
• Tongue: English
• Weight: 252 KB
• Volume: 42
• Category: Article
• ISSN: 0011-9059
• DOI: 10.1046/j.1365-4362.2003.01674_1.x

✦ Synopsis

A 2‐month‐old boy was seen at our pediatric dermatology department with a history of a tumoral lesion of the scalp since his birth. On examination he had a single, ovoid, firm, 2 × 1.8‐cm painless subcutaneous mass on the temporal left calvarium, covered by normal skin (Fig. 1). It had experienced explosive growth in the preceding 2 weeks. There was no history of previous trauma in the area. The remainder of the examination was normal. Roentgenographic studies of the skull revealed a soft‐tissue mass without involvement of the underlying bone. Ultrasonography of the lesion showed it to be an echolucid tumor. With the presumed diagnosis of dermoid cyst we sent the patient for surgical removal. At surgery, the lesion did not have the typical surgical appearance of a cyst. The histopathologic exam of the specimen was interpreted as cranial fasciitis of childhood (Fig. 2). Immunohistochemistry showed diffuse positivity for vimentin and muscle actin. After 1 year the patient is free of lesions.

Lesion at the temporal left calvarium

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Proliferation of loosely arranged spindle cells in a loose myxoid stroma (H&E stain, × 40)

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