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Congenital Generalized Lipodystrophy with Insulin Receptor Disorders

✍ Scribed by Soichi Kodama; Atsushi Seki; Michindo Ninomiya; Takashi Sakurai; Yorihiko Morishita; Masafumi Matsuo; Tamotsu Matsuo


Book ID
118710283
Publisher
John Wiley and Sons
Year
1977
Tongue
English
Weight
45 KB
Volume
19
Category
Article
ISSN
1328-8067

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Congenital generalized lipodystrophy wit
✍ Soichi Kodama; Masato Kasuga; Atsushi Seki; Michindo Ninomiya; Takashi Sakurai; πŸ“‚ Article πŸ“… 1978 πŸ› Springer 🌐 English βš– 481 KB

Hyperglycemia, glucose intolerance, hyperinsulinemia and resistance to exogenous insulin were found in a 10-year-old Japanese boy diagnosed as having congenital generalized lipodystrophy. Studies on insulin receptors of circulating mononuclear leucocytes indicated that insulin-resistant diabetes co