𝔖 Bobbio Scriptorium
✦   LIBER   ✦

Childhood Bullous Pemphigoid in Association with Hyperimmunoglobulin E Syndrome

✍ Scribed by Zulal Erbagci

Book ID
109090495
Publisher
John Wiley and Sons
Year
2008
Tongue
English
Weight
318 KB
Volume
25
Category
Article
ISSN
0736-8046

No coin nor oath required. For personal study only.

✦ Synopsis

Abstract: Bullous pemphigoid is an acquired immunobullous disorder affecting predominantly the elderly. It is very rare in children and exceptional in infants. Hyperimmunoglobulin E syndrome is a rare primary immunodeficiency characterized by a triad of high serum levels of polyclonal immunoglobulin E with peripheral eosinophilia, recurrent staphylococcal infections of the skin and lungs, and pruritic dermatitis. Variable associated features include coarse facies, cold cutaneous abscesses, and osteopenia. This report describes, to the best of my knowledge, the first instance of childhood bullous pemphigoid associated with hyperimmunoglobulin E syndrome in a 6‐month‐old boy.

πŸ“œ SIMILAR VOLUMES

Bullous pemphigoid in association with c
Bullous pemphigoid in association with cutaneous lesions specific to a myelodysplastic syndrome
✍ P. MODIANO; S. REICHERT; A. BARBAUD; P. BERNARD; M. WEBER; J.L. SCHMUTZ πŸ“‚ Article πŸ“… 1997 πŸ› John Wiley and Sons 🌐 English βš– 973 KB

Specific cutaneous lesions are a rare occurrence in myelodysplastic syndromes (MDS). The concurrent association of blistering skin lesions similar to those in bullous pemphigoid (BP), even though a rare event, suggests that BP may be a paraneoplastic syndrome. We report an 86-year-old man who had a

Childhood bullous pemphigoid associated
Childhood bullous pemphigoid associated with IgA antibodies against BP180 or BP230 antigens
✍ ARECHALDE; BRAUN; CALZA; HERTL; DIDIERJEAN; SAURAT; BORRADORI πŸ“‚ Article πŸ“… 1999 πŸ› John Wiley and Sons 🌐 English βš– 473 KB

Linear IgA bullous dermatosis (LABD) comprises a heterogeneous group of subepidermal blistering disorders characterized by in situ bound IgA antibodies in epidermal basement membrane. We report three children presenting clinical and immunopathological features characteristic of LABD. By immunoblotti

Eosinophilic spongiosis in association w
Eosinophilic spongiosis in association with bullous pemphigoid and chronic lymphocytic leukaemia
✍ M. Ameen; A.C. Pembroke; M.M. Black; R. Russell-Jones πŸ“‚ Article πŸ“… 2000 πŸ› John Wiley and Sons 🌐 English βš– 523 KB

We report the onset of an unusual blistering eruption following a diagnosis of B-cell chronic lymphocytic leukaemia (CLL). The histology consistently showed eosinophilic spongiosis, but the diagnosis of bullous pemphigoid was only confirmed after 13 years by repeated immunofluorescence studies. The