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Bone collagen aggregation abnormalities in osteogenesis imperfecta

✍ Scribed by Steven L. Teitelbaum; William J. Kraft; Robert Lang; Louis V. Avioli


Book ID
110551913
Publisher
Springer
Year
1974
Tongue
English
Weight
742 KB
Volume
17
Category
Article
ISSN
1432-0827

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Unexpected ultrastructral changes in bon
✍ Padmini Sarathchandra; F. Michael Pope πŸ“‚ Article πŸ“… 2005 πŸ› Elsevier Science 🌐 English βš– 564 KB

Osteogenesis Imperfecta (OI) is a heterogeneous, inherited bone disorder usually resulting from a defect in collagen synthesis or function. The Sillence classification recognises four OI subtypes of which type III is the severe, progressively deforming form. Here, we report distinctive ultrastructur