๐”– Bobbio Scriptorium
โœฆ   LIBER   โœฆ

Biochemistry and bioenergetics of glutaryl-CoA dehydrogenase deficiency

โœ Scribed by S. W. Sauer

Publisher
Springer
Year
2007
Tongue
English
Weight
431 KB
Volume
30
Category
Article
ISSN
0141-8955

No coin nor oath required. For personal study only.

๐Ÿ“œ SIMILAR VOLUMES

Pathomechanisms of neurodegeneration in
Pathomechanisms of neurodegeneration in glutaryl-CoA dehydrogenase deficiency
โœ Stefan Kรถlker; David M. Koeller; Jรผrgen G. Okun; Georg F. Hoffmann ๐Ÿ“‚ Article ๐Ÿ“… 2003 ๐Ÿ› John Wiley and Sons ๐ŸŒ English โš– 186 KB

## Abstract Glutarylโ€CoA dehydrogenase deficiency is an inherited organic aciduria with predominantly neurological presentation. Biochemically, it is characterized by an accumulation and enhanced urinary excretion of two key organic acids, glutaric acid and 3โ€hydroxyglutaric acid. If untreated, acu

Synthesis of Substrate Analogs for Gluta
Synthesis of Substrate Analogs for Glutaryl-CoA Dehydrogenase: 3-Thia-Glutaryl-CoA and 4-Nitrobutyryl-CoA
โœ Patricia L. Kultgen; Leonard Edwards; Jr.; Colleen M. Byron ๐Ÿ“‚ Article ๐Ÿ“… 1997 ๐Ÿ› Elsevier Science ๐ŸŒ English โš– 67 KB

We report the newly successful synthesis of 3-thia-glutaryl-CoA and a partial synthesis of 4-nitrobutyryl-CoA, substrate analogs to glutaryl-CoA dehydrogenase (GCD), an enzyme utilized by mammals and by bacteria in the metabolism of the amino acids L-tryptophan, L-lysine, and L-hydroxylysine. Using