Molecular and phenotypic heterogeneity i
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Ute Spiekerkoetter; Bin Sun; Zaza Khuchua; Michael J. Bennett; Arnold W. Strauss
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Article
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2003
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John Wiley and Sons
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English
β 241 KB
The mitochondrial trifunctional protein (TFP) is a multienzyme complex of the fatty acid beta-oxidation cycle. It is composed of four alpha-subunits (HADHA) harboring long-chain enoyl-CoA hydratase and long-chain L-3-hydroxyacyl-CoA dehydrogenase (LCHAD) and four beta-subunits (HADHB) harboring long