✦ LIBER ✦

Bilateral pulmonary agenesis: Association with the hydrolethalus syndrome and review of the literature from a developmental field perspective

✍ Scribed by Toriello, Helga V. ;Bauserman, Stephen C. ;Opitz, John M. ;Reynolds, James F.

Publisher: John Wiley and Sons
Year: 1985
Tongue: English
Weight: 546 KB
Volume: 21
Category: Article
ISSN: 0148-7299
DOI: 10.1002/ajmg.1320210114

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✦ Synopsis

Only a few cases of bilateral pulmonary agenesis have been reported. Recently we saw such a case in an infant with the hydrolethalus syndrome. This observation seems to indicate that bilateral pulmonary agenesis is a severe expression of a developmental field defect that usually is represented by abnormal lung lobation or hypoplasia. The previously reported cases are discussed from the perspective of the developmental field concept.

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