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Benign hereditary chorea—Entity or syndrome?

✍ Scribed by Anette Schrag; Niall P. Quinn; Kailash P. Bhatia; C. David Marsden

Publisher
John Wiley and Sons
Year
2000
Tongue
English
Weight
57 KB
Volume
15
Category
Article
ISSN
0885-3185

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Snmmerp: Benign hereditary chorea (BHC) is an autosomal dominant disorder characterized by chorea of early onset with little or no progression. There is marked clinical variability in this disease with some subjects having onset in infancy and others with onset in early adulthood. In contrast to Hun