In an attempt to elucidate the pathogenesis of focal cytochrome c-oxidase (COX) deficiency in skeletal muscle from patients with chronic progressive external ophthalmoplegia (CPEO), we examined the longitudinal distribution of COX activity in single muscle fibers from 6 CPEO patients with muscle mit
β¦ LIBER β¦
Beneficial effect of sodium dichloroacetate in muscle cytochrome C oxidase deficiency
β Scribed by A. B. Burlina; O. Milanesi; P. Biban; A. Bordugo; B. Garavaglia; F. Zacchello; S. Di Mauro
- Publisher
- Springer
- Year
- 1993
- Tongue
- English
- Weight
- 152 KB
- Volume
- 152
- Category
- Article
- ISSN
- 0340-6997
No coin nor oath required. For personal study only.
π SIMILAR VOLUMES
Segmental cytochrome c-oxidase deficienc
β
Dr. Taro Matsuoka; Dr. Yu-Ichi Goto; Dr. Hitomi Hasegawa; Ikuya Nonaka
π
Article
π
1992
π
John Wiley and Sons
π
English
β 576 KB
Cytochrome-C-oxidase deficiency in muscl
β
M. Rimoldi; E. Bottacchi; L. Rossi; F. Cornelio; G. Uziel; S. Donato
π
Article
π
1982
π
Springer
π
English
β 554 KB
Deficiency of cytochromes b and aa3in mu
Deficiency of cytochromes b and aa3in muscle from a floppy infant with cytochrome oxidase deficiency
β
R. C. A. Sengers; J. M. F. Trijbels; J. A. J. M. Bakkeren; W. Ruitenbeek; J. C.
π
Article
π
1984
π
Springer
π
English
β 986 KB
A girl was presented suffering from generalised weakness and cardiorespiratory insufficiency. She succumbed at the age of 5 months. Lactate levels were elevated in serum, cerebrospinal fluid and urine. Histopathological examination revealed a mitochondrial myopathy. In muscle tissue the cytochrome o
Expression of the alternative oxidase co
β
Emmanuel P. Dassa; Eric Dufour; SΓ©rgio GonΓ§alves; Vincent Paupe; Gertjan A. J. H
π
Article
π
2009
π
John Wiley and Sons
π
English
β 464 KB
Effect of hypothyroidism on the expressi
β
Rebecca J. Stevens; Mary L. Nishio; David A. Hood
π
Article
π
1995
π
Springer
π
English
β 822 KB
Liver cytochrome c oxidase deficiency in
β
Patrick Edery; Bénédicte Gérard; Dominique Chretien; Agnès Râtig; Roberto Cerron
π
Article
π
1994
π
Springer
π
English
β 796 KB