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Beckwith–Weidemann syndrome: partial glossectomy

✍ Scribed by B. Beltrán Salinas; L. Melloni; D. Perez Infante


Book ID
116562872
Publisher
Elsevier Science
Year
2011
Tongue
English
Weight
101 KB
Volume
40
Category
Article
ISSN
0901-5027

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## Abstract Neurobehavioral defects have been reported in human imprinting disorders such as Prader–Willi syndrome and Angelman syndrome and imprinted genes are often implicated in neurodevelopment processes. Beckwith–Wiedemann syndrome (BWS) is a classical human imprinting disorder characterized b