Alveolar soft-part sarcoma

✍ Scribed by Raney, R. Beverly

• Publisher: John Wiley and Sons
• Year: 1979
• Tongue: English
• Weight: 582 KB
• Volume: 6
• Category: Article
• ISSN: 0098-1532
• DOI: 10.1002/mpo.2950060414

✦ Synopsis

The patient is a three-and-one-half-year-old girl who was well until three weeks prior to referral when her mother noticed a small subcutaneous mass below the left scapula. There was no history of trauma, and neither pain, fever, nor regional adenopathy was noted by the examining surgeon. At surgery, a 3 X 3 cm mass was found in the left latissimus dorsi muscle. Excisional biopsy was performed, and a specimen examined by frozen section was reported as consistent with a sarcoma of soft tissue. Wide local excision was then performed under the same general anesthetic, and no tumor was found in the second specimen or at its margins. The permanent sections showed a malignant alveolar soft-part sarcoma. The child was referred to the Children's Hospital of Philadelphia for further studies and management.

On physical examination, the child was a healthy-appearing girl of the stated age with a well-healed scar below the left scapula. There was no nodularity in the wound area and no adenopathy. Except for the scar, the physical examination was within normal limits. The complete blood count and urinalysis were also normal.