Aicardi–Goutières syndrome (AGS)
✍
John B.P. Stephenson
📂
Article
📅
2008
🏛
Elsevier Science
🌐
English
⚖ 271 KB
In 1984, Jean Aicardi and Françoise Goutières described 8 children showing both severe brain atrophy and chronic cerebrospinal fluid lymphocytosis, with basal ganglia calcification in at least one member of each affected family. The course was rapid to death or a vegetative outcome. Aicardi and Gout