Advances in understanding the pathogenes
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Usmani, G. Naheed; Woda, Bruce A.; Newburger, Peter E.
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Article
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2013
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John Wiley and Sons
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English
β 367 KB
## Summary Haemophagocytic lymphohistiocytosis (HLH) is a hyperinflammatory disorder resulting from immune dysfunction reflecting either primary immune deficiency or acquired failure of normal immune homeostasis. Familial HLH includes autosomal recessive and Xβlinked disorders characterized by unco