Advances in diagnosis and treatment in patients with pulmonary arterial hypertension
β Scribed by Myung H. Park
- Publisher
- John Wiley and Sons
- Year
- 2008
- Tongue
- English
- Weight
- 108 KB
- Volume
- 71
- Category
- Article
- ISSN
- 1522-1946
No coin nor oath required. For personal study only.
π SIMILAR VOLUMES
The etiology of scleroderma remains unknown. However, it is believed that the vascular lesions found in involved organs have a pathogenesis related to endothelial cell injury (1). Pulmonary hypertension is the most common cause of acute dyspnea in patients with systemic sclerosis and is thought to
## Abstract ## Objective Lung transplantation is a viable, lifeβsaving intervention for several primary pulmonary disorders complicated by severe lung dysfunction. This study was undertaken to evaluate whether patients with systemic sclerosis (scleroderma), a systemic autoimmune rheumatic disorder
## Abstract Pulmonary arterial hypertension (PAH) and hereditary hemorrhagic telangiectasia (HHT) are distinct clinical entities caused by germline mutations in genes encoding members of the TGFΞ²/BMP superfamily: __BMPR2__ in PAH and __ACVRL1__, __ENG__, or __SMAD4__ in HHT. When PAH and HHT occasi