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Adductor laryngeal breathing dystonia in a patient with lubag (X-linked dystonia-parkinsonism syndrome)

✍ Scribed by Dr. M. F. Lew; M. Shindo; C. B. Moskowitz; K. C. Wilhelmsen; S. Fahn; C. H. Waters

Publisher: John Wiley and Sons
Year: 1994
Tongue: English
Weight: 308 KB
Volume: 9
Category: Article
ISSN: 0885-3185
DOI: 10.1002/mds.870090307

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✦ Synopsis

Abstract

We report a patient with Lubag (X‐linked dystonia‐parkinsonism) who presented with severe respiratory stridor form adductor laryngeal breathing dystonia. Emergency tracheostomy was necessary, and subsequent laryngeal injection with botulinum toxin led to worsening aspiration. Botulinum toxin injection for severe lingual dystonia was successful.

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