Acquired pseudoxanthoma elasticum presenting after liver transplantation
โ Scribed by Lionel Bercovitch; Ludovic Martin; Nicolas Chassaing; Timothy W. Hefferon; Didier Bessis; Olivier Vanakker; Sharon F. Terry
- Book ID
- 116586830
- Publisher
- Elsevier Science
- Year
- 2011
- Tongue
- English
- Weight
- 377 KB
- Volume
- 64
- Category
- Article
- ISSN
- 1097-6787
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๐ SIMILAR VOLUMES
We report a 48-year-old man presenting with refractory hyperammonemia after orthotopic liver transplantation. On investigation he was found to have acquired hepatic glutamine synthetase deficiency, a rare condition that occurs after organ transplantations. The patient was started on continuous venov
The liver's role as the largest organ of metabolism and the unique and often critical function of liver-specific enzyme pathways imply a greater risk to the recipient of acquiring a donor metabolic disease with liver transplants versus other solid organ transplants. With clinical consequences rarely