𝔖 Bobbio Scriptorium
✦   LIBER   ✦

Absence of PITX2, BARX1, and FOXC1 mutations in De Hauwere syndrome (Axenfeld–Rieger anomaly, hydrocephaly, hearing loss): A 25-year follow up

✍ Scribed by R. Brian Lowry; Douglas B. Gould; Michael A. Walter; Paul R. Savage


Publisher
John Wiley and Sons
Year
2007
Tongue
English
Weight
148 KB
Volume
143A
Category
Article
ISSN
1552-4825

No coin nor oath required. For personal study only.

✦ Synopsis


Abstract

This study reports a 25‐year follow‐up of a patient with De Hauwere syndrome (Axenfeld–Rieger anomaly, hydrocephalus, and hearing loss) whose intelligence is normal. Short stature and hyperlaxity of joints later leading to severe joint pain were noted. Mutation analysis of candidate genes known or suspected to be associated with Axenfeld–Rieger eye malformations was performed. This included complete sequencing for PITX2, BARX1 and the forkhead domain of FOXC1. The results of these analyses were negative and suggest that De Hauwere syndrome is caused by a different gene. © 2007 Wiley‐Liss, Inc.