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Abnormal hepatobiliary and circulating lipid metabolism in the Long-Evans Cinnamon rat model of Wilson's disease

✍ Scribed by Emile Levy; Sylvain Brunet; Fernando Alvarez; Ernest Seidman; Guylaine Bouchard; Enrique Escobar; Steve Martin


Book ID
116718997
Publisher
Elsevier Science
Year
2007
Tongue
English
Weight
870 KB
Volume
80
Category
Article
ISSN
0024-3205

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The disposition behaviors and de-coppering effect of triethylenetetramine dihydrochloride (trientine), a selective chelating agent for copper and an 'orphan drug' for Wilson's disease, have been evaluated in an animal model, Long-Evans Cinnamon (LEC) rats, and normal rats (Wistar). In LEC rats, urin