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Abnormal arylsulphatase activities of fibroblasts cultured from patients with mucopolysaccharidosis and cystinosis

✍ Scribed by Furusho, K. ;Vetrella, M. ;Latta, E.

Publisher
Springer-Verlag
Year
1971
Weight
454 KB
Volume
110
Category
Article
ISSN
0044-2917

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✦ Synopsis

The activity of arylsulphatases A and B was studied in cultured fibroblasts of 2 patients with Hurler's syndrome, 2 patients with Hunter's syndrome and 2 patients with eystinosis.

The activity of arylsulphatase A was found to be lower in fibroblasts in patients with Hurler's syndrome than in the controls while it was not always decreased in Hunter's syndrome. The activity of arylsulphatase B was increased in fibroblasts in Hunter's syndrome. In eystinosis the activity of arylsulphatase 13 was selectively decreased in fibroblasts.

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