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A novel assay for lysosomal pepstatin-insensitive proteinase and its application for the diagnosis of late-infantile neuronal ceroid lipofuscinosis

✍ Scribed by Mohammed A. Junaid; Susan Sklower Brooks; Krystyna E. Wisniewski; Raju K. Pullarkat


Book ID
117460852
Publisher
Elsevier Science
Year
1999
Tongue
English
Weight
78 KB
Volume
281
Category
Article
ISSN
0009-8981

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## Diagnosis of late-infantile neuronal ceroid lipofuscinosis: A new sensitive method to assay lysosomal pepstatin-insensitive proteinase activity in human and animal specimens by capillary electrophoresis Batten disease, or human late-infantile neuronal ceroid lipofuscinosis (LINCL) is a familiar