Diagnosis of late-infantile neuronal cer
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Simona Viglio; Elaine Marchi; Krystyna Wisniewski; BegΓ΅na Casado; Giuseppe Cetta
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Article
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2001
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John Wiley and Sons
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English
β 114 KB
π 2 views
## Diagnosis of late-infantile neuronal ceroid lipofuscinosis: A new sensitive method to assay lysosomal pepstatin-insensitive proteinase activity in human and animal specimens by capillary electrophoresis Batten disease, or human late-infantile neuronal ceroid lipofuscinosis (LINCL) is a familiar